Prepared by David S. Wolf, MD, Starr Borden, MD, and Herbert L. Fred, MD, The University of Texas Health Science Center, Houston

This 42-year-old woman presented with life-long hypertrophy of the entire left half of her body. Particularly striking were the left upper torso (Figure 1), arm (Figure 2), and hand (Figure 3). She also had a large port wine hemangioma on her back (Figure 1), and small, superficial varicosities in her left leg. Her family history was unremarkable.

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